Síndrome de reperfusión pulmonar tras implante de stents pulmonares en un paciente con síndrome de tortuosidad vascular [caso clínico]
Por: Berenguer Potenciano, María [Pediatría] | Piris Borregas, Salvador [Pediatría] | Mendoza Soto, Alberto [Pediatría] | Velasco Bayón, José Manuel [Cardiología] | Caro Barri, Ana [Pediatría].
Colaborador(es): Servicio de Pediatría-Neonatología.
Tipo de material: ArtículoEditor: Anales de pediatría (Barcelona, Spain:2003). 2015Descripción: 82(1):e17-20.Recursos en línea: Solicitar documento Resumen: Vascular tortuosity syndrome is a rare genetic disorder that causes tortuosity and stenosis of the pulmonary, systemic and / or coronary circulations. As a result of treatment of pulmonary stenosis, symptoms of pulmonary edema, known as lung reperfusion syndrome, may occur. The case is presented of an adolescent patient with vascular tortuosity syndrome who presented with a pulmonary reperfusion syndrome after multiple stent implants in the left pulmonary artery. After the procedure, the patient immediately developed an acute pulmonary edema with severe clinical deterioration, which required assistance with extracorporeal membrane oxygenation for recovery.Tipo de ítem | Ubicación actual | Signatura | Estado | Fecha de vencimiento |
---|---|---|---|---|
Caso clínico | PC17286 (Navegar estantería) | Disponible |
Formato Vancouver:
Berenguer Potenciano M, Piris Borregas S, Mendoza Soto A, Velasco Bayón JM, Caro Barri A. Síndrome de reperfusión pulmonar tras implante de stents pulmonares en un paciente con síndrome de tortuosidad vascular. An Pediatr (Barc). 2015 Jan;82(1):e17-20.
PMID: 25082128
Contiene 12 referencias
Vascular tortuosity syndrome is a rare genetic disorder that causes tortuosity and stenosis of the pulmonary, systemic and / or coronary circulations. As a result of treatment of pulmonary stenosis, symptoms of pulmonary edema, known as lung reperfusion syndrome, may occur. The case is presented of an adolescent patient with vascular tortuosity syndrome who presented with a pulmonary reperfusion syndrome after multiple stent implants in the left pulmonary artery. After the procedure, the patient immediately developed an acute pulmonary edema with severe clinical deterioration, which required assistance with extracorporeal membrane oxygenation for recovery.
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