000 nab a22 7a 4500
999 _c17286
_d17286
003 PC17286
005 20230309130426.0
008 230309b xxu||||| |||| 00| 0 eng d
040 _cH12O
041 _aspa
100 _93115
_aBerenguer Potenciano, María
_ePediatría
100 _92844
_aPiris Borregas, Salvador
_ePediatría
100 _9849
_aMendoza Soto, Alberto
_ePediatría
100 _9850
_aVelasco Bayón, José Manuel
_eCardiología
100 _93204
_aCaro Barri, Ana
_ePediatría
245 0 0 _a Síndrome de reperfusión pulmonar tras implante de stents pulmonares en un paciente con síndrome de tortuosidad vascular
_h[caso clínico]
260 _bAnales de pediatría (Barcelona, Spain:2003).
_c2015
300 _a82(1):e17-20.
500 _aFormato Vancouver: Berenguer Potenciano M, Piris Borregas S, Mendoza Soto A, Velasco Bayón JM, Caro Barri A. Síndrome de reperfusión pulmonar tras implante de stents pulmonares en un paciente con síndrome de tortuosidad vascular. An Pediatr (Barc). 2015 Jan;82(1):e17-20.
501 _aPMID: 25082128
504 _aContiene 12 referencias
520 _aVascular tortuosity syndrome is a rare genetic disorder that causes tortuosity and stenosis of the pulmonary, systemic and / or coronary circulations. As a result of treatment of pulmonary stenosis, symptoms of pulmonary edema, known as lung reperfusion syndrome, may occur. The case is presented of an adolescent patient with vascular tortuosity syndrome who presented with a pulmonary reperfusion syndrome after multiple stent implants in the left pulmonary artery. After the procedure, the patient immediately developed an acute pulmonary edema with severe clinical deterioration, which required assistance with extracorporeal membrane oxygenation for recovery.
710 _9446
_aServicio de Pediatría-Neonatología
856 _uhttp://pc-h12o-es.m-hdoct.a17.csinet.es/pdf/pc/1/pc17286.pdf
_ySolicitar documento
942 _2ddc
_cCAS
_n0